Morquio disease, type A natural cures |
Morquio disease, type A Definition
Referred to as mucopolysaccharidosis IV or Morquio, the disorder is known to be an autosomal recessive mucopolysaccharide disease that is usually inherited. It is also considered a relatively rare case of dwarfism with serious consequences. This happens when the body cannot process certain types of mucopplysaccharides, then they just build up or are eliminated causing a range of symptoms. The type A form is a deficiency of the enzyme N-acetylgalactosamine-6-sulfate sulfatase.
Morquio disease, type A Diagnosis
Physical examination may reveal abnormal curving of the spine or kyphoscoliosis, cloudy cornea, heart murmur, inquinal hernia, liver enlargement, loss of nerve function below the neck and short physique. Other tests may also be composed of blood culture, echocardiogram, genetic testing, hearing test, slit-lamp eye exam, skin fibrolast culture, and x-rays of the long bones, ribs and spine.
Morquio disease, type A Treatment
There are no current treatments for the disease. Only palliative procedures are available to manage Morquio syndrome patients. Most physicians also recommend cervical spine fusion to affected patients since all of those with the disorder have odontoid hypoplasia that can lead to atlanoaxial subluxation.
Morquio disease, type A Symptoms and Signs
Morquio syndrome has an assortment of symptoms. Among them are abnormal heart development, abnormal skeletal development, hypermobile joints, large fingers, knock-knees, widely spaced teeth, large head, bell shaped chest, compression of spinal cord, enlarged heart, and dwarfism.
Morquio disease, type A Causes
A deficiency in the enzyme N-acetylgalactosamine-6-sulfate sulfatase causes Type A Morquio syndrome.
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Morquio disease, type A by state |
Morquio disease, type A in Alabama
Morquio disease, type A in Alaska
Morquio disease, type A in Arizona
Morquio disease, type A in Arkansas
Morquio disease, type A in Armed Forces
Morquio disease, type A in California
Morquio disease, type A in Colorado
Morquio disease, type A in Connecticut
Morquio disease, type A in Delaware
Morquio disease, type A in District of Columbia
Morquio disease, type A in Florida
Morquio disease, type A in Georgia
Morquio disease, type A in Hawaii
Morquio disease, type A in Idaho
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Morquio disease, type A in Iowa
Morquio disease, type A in Kansas
Morquio disease, type A in Kentucky
Morquio disease, type A in Louisiana
Morquio disease, type A in Maine
Morquio disease, type A in Maryland
Morquio disease, type A in Massachusetts
Morquio disease, type A in Michigan
Morquio disease, type A in Minnesota
Morquio disease, type A in Mississippi
Morquio disease, type A in Missouri
Morquio disease, type A in Montana
Morquio disease, type A in Nebraska
Morquio disease, type A in Nevada
Morquio disease, type A in New Hampshire
Morquio disease, type A in New Jersey
Morquio disease, type A in New Mexico
Morquio disease, type A in New York
Morquio disease, type A in North Carolina
Morquio disease, type A in North Dakota
Morquio disease, type A in Ohio
Morquio disease, type A in Oklahoma
Morquio disease, type A in Oregon
Morquio disease, type A in Pennsylvania
Morquio disease, type A in Puerto Rico
Morquio disease, type A in Rhode Island
Morquio disease, type A in South Carolina
Morquio disease, type A in South Dakota
Morquio disease, type A in Tennessee
Morquio disease, type A in Texas
Morquio disease, type A in Utah
Morquio disease, type A in Vermont
Morquio disease, type A in Virginia
Morquio disease, type A in Washington
Morquio disease, type A in West Virginia
Morquio disease, type A in Wisconsin
Morquio disease, type A in Wyoming
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