Medium-chain Acyl-CoA dehydrogenase deficiency natural cures

Medium-chain Acyl-CoA dehydrogenase deficiency Definition

By definition, this deficiency is a fatty acid oxidation disorder that is connected with inborn errors of metabolism errors that occur at birth The defect is found in the enzyme complex called medium-chain acyl dehydrogenase (MCAD) whose ability to function efficiently is reduced significantly. The disorder has also been known to cause (rarely) Sudden infant death syndrome or SIDS.

Medium-chain Acyl-CoA dehydrogenase deficiency Diagnosis

Diagnosis is usually focused on resulting complications the impairment of fatty acid oxidation.

Medium-chain Acyl-CoA dehydrogenase deficiency Treatment

There is no cure for the deficiency but its adverse effects can be prevented by proper health management. Patients with the disorder should have adequate energy levels which mean no lengthy fasting. Lack of appetite caused by other illnesses or conditions makes it necessary for intravenous glucose to prevent the body from depending on fatty acids for energy. Patients with the disorder should stick to a low-fat diet. The taking of carnitine supplements have been shown to be effective in arresting toxic accumulation of fatty acids

Medium-chain Acyl-CoA dehydrogenase deficiency Symptoms and Signs

Significant symptoms manifest when the disorder deteriorates into fatty acid buildup, and metabolic conditions such as hypoglycemia and hyperammonemia. When this happens, typical symptoms include vomiting and extreme lethargy.

Medium-chain Acyl-CoA dehydrogenase deficiency Causes
The main cause of MCAD is genetic; mutations in the gene can cause insufficient levels of the medium-chain acyl-coenzyme. Being inherited, the condition follows an autosomal recessive pattern in which two copies of the defective gene in each cell are required for MCAD to be inherited; one inherited copy of the faulty gene means an individual becoming a carrier.


Medium-chain Acyl-CoA dehydrogenase deficiency by state

Medium-chain Acyl-CoA dehydrogenase deficiency in Alabama
Medium-chain Acyl-CoA dehydrogenase deficiency in Alaska
Medium-chain Acyl-CoA dehydrogenase deficiency in Arizona
Medium-chain Acyl-CoA dehydrogenase deficiency in Arkansas
Medium-chain Acyl-CoA dehydrogenase deficiency in Armed Forces
Medium-chain Acyl-CoA dehydrogenase deficiency in California
Medium-chain Acyl-CoA dehydrogenase deficiency in Colorado
Medium-chain Acyl-CoA dehydrogenase deficiency in Connecticut
Medium-chain Acyl-CoA dehydrogenase deficiency in Delaware
Medium-chain Acyl-CoA dehydrogenase deficiency in District of Columbia
Medium-chain Acyl-CoA dehydrogenase deficiency in Florida
Medium-chain Acyl-CoA dehydrogenase deficiency in Georgia
Medium-chain Acyl-CoA dehydrogenase deficiency in Hawaii
Medium-chain Acyl-CoA dehydrogenase deficiency in Idaho
Medium-chain Acyl-CoA dehydrogenase deficiency in Illinois
Medium-chain Acyl-CoA dehydrogenase deficiency in Indiana
Medium-chain Acyl-CoA dehydrogenase deficiency in Iowa
Medium-chain Acyl-CoA dehydrogenase deficiency in Kansas
Medium-chain Acyl-CoA dehydrogenase deficiency in Kentucky
Medium-chain Acyl-CoA dehydrogenase deficiency in Louisiana
Medium-chain Acyl-CoA dehydrogenase deficiency in Maine
Medium-chain Acyl-CoA dehydrogenase deficiency in Maryland
Medium-chain Acyl-CoA dehydrogenase deficiency in Massachusetts
Medium-chain Acyl-CoA dehydrogenase deficiency in Michigan
Medium-chain Acyl-CoA dehydrogenase deficiency in Minnesota
Medium-chain Acyl-CoA dehydrogenase deficiency in Mississippi
Medium-chain Acyl-CoA dehydrogenase deficiency in Missouri
Medium-chain Acyl-CoA dehydrogenase deficiency in Montana
Medium-chain Acyl-CoA dehydrogenase deficiency in Nebraska
Medium-chain Acyl-CoA dehydrogenase deficiency in Nevada
Medium-chain Acyl-CoA dehydrogenase deficiency in New Hampshire
Medium-chain Acyl-CoA dehydrogenase deficiency in New Jersey
Medium-chain Acyl-CoA dehydrogenase deficiency in New Mexico
Medium-chain Acyl-CoA dehydrogenase deficiency in New York
Medium-chain Acyl-CoA dehydrogenase deficiency in North Carolina
Medium-chain Acyl-CoA dehydrogenase deficiency in North Dakota
Medium-chain Acyl-CoA dehydrogenase deficiency in Ohio
Medium-chain Acyl-CoA dehydrogenase deficiency in Oklahoma
Medium-chain Acyl-CoA dehydrogenase deficiency in Oregon
Medium-chain Acyl-CoA dehydrogenase deficiency in Pennsylvania
Medium-chain Acyl-CoA dehydrogenase deficiency in Puerto Rico
Medium-chain Acyl-CoA dehydrogenase deficiency in Rhode Island
Medium-chain Acyl-CoA dehydrogenase deficiency in South Carolina
Medium-chain Acyl-CoA dehydrogenase deficiency in South Dakota
Medium-chain Acyl-CoA dehydrogenase deficiency in Tennessee
Medium-chain Acyl-CoA dehydrogenase deficiency in Texas
Medium-chain Acyl-CoA dehydrogenase deficiency in Utah
Medium-chain Acyl-CoA dehydrogenase deficiency in Vermont
Medium-chain Acyl-CoA dehydrogenase deficiency in Virginia
Medium-chain Acyl-CoA dehydrogenase deficiency in Washington
Medium-chain Acyl-CoA dehydrogenase deficiency in West Virginia
Medium-chain Acyl-CoA dehydrogenase deficiency in Wisconsin
Medium-chain Acyl-CoA dehydrogenase deficiency in Wyoming
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